Study note

Management of aortic dilatation risk in Marfan syndrome

THE CONTEXT
Management combines preventive drug treatment, activity advice and surgery for progressive aortic dilatation.

Medical treatment and activity

•
β-blockers or ARBs should be given to all patients with Marfan syndrome because they may reduce the risk of aortic dilatation.
•
Activities associated with increases in cardiac output are best avoided.

Surgical management

•
Aortic root replacement can be performed when aortic dilatation is progressive.
Explore this chapter
NEETx
Learn. Practise. Remember.